Patients with Hurler Syndrome (Complete Deficiency of α-L-Iduronidase) Have Mental

Multiple Choice

Patients with Hurler syndrome (complete deficiency of α-L-iduronidase) have mental deficiency in addition to physical deformities, corneal clouding, and valvular heart disease.Their mental deficiency is caused by the accumulation of:

A) α-L-iduronic acid.
B) Heparan sulfate.
C) Chondroitin sulfate.
D) Hyaluronic acid.
E) Keratan sulfate.