Question 1

If an infant has hydrops fetalis, which type of thalassemia does the nurse know this to be?

Accepted Answer

A)  Beta minor 
B)  Beta major 
C)  Alpha minor 
D)  Alpha major

Question 2

A 12-month-old toddler weighing 8 kilograms is brought to the clinic because of weakness, slow physical growth, and developmental delays. His mother reports that the only food he will consume is cow's milk. The symptoms support a diagnosis of which form of anemia?

Accepted Answer

A)  Pernicious 
B)  Iron deficiency 
C)  Aplastic 
D)  Hemolytic

Question 3

Testing reveals that a child has hemophilia A. This bleeding disorder results from a deficiency in factor:

Accepted Answer

A)  IX. 
B)  XII. 
C)  XIII. 
D)  VIII.

Question 4

A 2-year-old male presented with growth and maturation retardation and splenomegaly. He died shortly after arriving at the ER. Autopsy revealed thalassemia, a condition involving what feature?

Accepted Answer

A)  Defective erythrocyte membranes 
B)  Poor iron metabolism 
C)  Inappropriate stem cell formation 
D)  Defective hemoglobin synthesis

Question 5

A nurse is planning care for a child with iron deficiency anemia. Characteristics of iron deficiency anemia include which of the following? (Select all that apply.)

Accepted Answer

A)  It is most common between the ages of 6 months and 2 years. 
B)  It is related to gender and race. 
C)  It may be related to socioeconomic factors. 
D)  It is rare among teenagers. 
E)  It is difficult to diagnose in early stages.

Question 6

Autopsy on a stillborn fetus reveals cardiomegaly, hepatomegaly, edema, and ascites as well as fulminant intrauterine heart failure. Considering these findings, what is the most likely cause of death?

Accepted Answer

A)  Alpha thalassemia minor 
B)  Alpha thalassemia major 
C)  Hemoglobin H disease 
D)  Alpha trait

Question 7

What organ is responsible for removing sickled cells from circulation?

Accepted Answer

A)  The liver 
B)  The pancreas 
C)  The kidney 
D)  The spleen

Exam 22: Alterations of Hematological Function in Children